Hai cercato: 1-Deoxy-D-galactitol

Fornitore: Apollo Scientific

Descrizione: 1-Deoxy-D-galactitol 98+%

Fornitore: TCI EUROPE

Descrizione: Galactitol ≥98.0% (by GC)

Codice catalogo: (PHR1833-1G)

Fornitore: Merck

Codice articolo fornitore: PHR1833-1G

Codice articolo locale: SUPLPHR1833-1G

Descrizione: Organic Standard, Galactitol

UOM: 1 * 1 g

Promo

Fornitore: Thermo Scientific

Descrizione: Galactitol 99+%

MSDS

Codice catalogo: (APOSOR2365T-10MG)

Fornitore: Apollo Scientific

Codice articolo fornitore: OR2365T-10MG

Codice articolo locale: APOSOR2365T-10MG

Descrizione: Migalastat hydrochloride

UOM: 1 * 10 mg

Promo

Fornitore: Thermo Scientific

Descrizione: Galactitol ≥97%

MSDS Certificati

Codice catalogo: (BOSSBS-13267R-FITC)

Fornitore: Bioss

Codice articolo fornitore: BS-13267R-FITC

Codice articolo locale: BOSSBS-13267R-FITC

Descrizione: GALK2 is important in the first step of the galactose metabolism pathway. GALK1, which belongs to the GHMP kinase family of proteins, is a crucial enzyme for galactose metabolism, specifically converting ?d-galactose to galactose 1-phosphate. Defects in the gene encoding GALK1 can cause galactosemia II, an autosomal recessive disorder characterized by congenital cataracts during infancy, often within the first two weeks of life. In the adult population, galactosemia II can cause presenile cataracts that are secondary to accumulation of galactitol in the lens of the eye. A second gene, GALK2, encodes an enzyme with greater activity against GalNAc than galactose. GALK2 has been implicated in the salvage pathway for the reutilization of free GalNAc derived from the degradation of complex carbohydrates.

UOM: 1 * 100 µl

Promo

Codice catalogo: (BOSSBS-13267R-HRP)

Fornitore: Bioss

Codice articolo fornitore: BS-13267R-HRP

Codice articolo locale: BOSSBS-13267R-HRP

Descrizione: GALK2 is important in the first step of the galactose metabolism pathway. GALK1, which belongs to the GHMP kinase family of proteins, is a crucial enzyme for galactose metabolism, specifically converting ?d-galactose to galactose 1-phosphate. Defects in the gene encoding GALK1 can cause galactosemia II, an autosomal recessive disorder characterized by congenital cataracts during infancy, often within the first two weeks of life. In the adult population, galactosemia II can cause presenile cataracts that are secondary to accumulation of galactitol in the lens of the eye. A second gene, GALK2, encodes an enzyme with greater activity against GalNAc than galactose. GALK2 has been implicated in the salvage pathway for the reutilization of free GalNAc derived from the degradation of complex carbohydrates.

UOM: 1 * 100 µl

Promo

Codice catalogo: (BOSSBS-13267R-CY3)

Fornitore: Bioss

Codice articolo fornitore: BS-13267R-CY3

Codice articolo locale: BOSSBS-13267R-CY3

Descrizione: GALK2 is important in the first step of the galactose metabolism pathway. GALK1, which belongs to the GHMP kinase family of proteins, is a crucial enzyme for galactose metabolism, specifically converting ?d-galactose to galactose 1-phosphate. Defects in the gene encoding GALK1 can cause galactosemia II, an autosomal recessive disorder characterized by congenital cataracts during infancy, often within the first two weeks of life. In the adult population, galactosemia II can cause presenile cataracts that are secondary to accumulation of galactitol in the lens of the eye. A second gene, GALK2, encodes an enzyme with greater activity against GalNAc than galactose. GALK2 has been implicated in the salvage pathway for the reutilization of free GalNAc derived from the degradation of complex carbohydrates.

UOM: 1 * 100 µl

Promo

Codice catalogo: (BOSSBS-13267R-CY5)

Fornitore: Bioss

Codice articolo fornitore: BS-13267R-CY5

Codice articolo locale: BOSSBS-13267R-CY5

Descrizione: GALK2 is important in the first step of the galactose metabolism pathway. GALK1, which belongs to the GHMP kinase family of proteins, is a crucial enzyme for galactose metabolism, specifically converting ?d-galactose to galactose 1-phosphate. Defects in the gene encoding GALK1 can cause galactosemia II, an autosomal recessive disorder characterized by congenital cataracts during infancy, often within the first two weeks of life. In the adult population, galactosemia II can cause presenile cataracts that are secondary to accumulation of galactitol in the lens of the eye. A second gene, GALK2, encodes an enzyme with greater activity against GalNAc than galactose. GALK2 has been implicated in the salvage pathway for the reutilization of free GalNAc derived from the degradation of complex carbohydrates.

UOM: 1 * 100 µl

Promo

Codice catalogo: (1287711.)

Fornitore: USP

Codice articolo fornitore: 1287711

Codice articolo locale: USPH1287711

Descrizione: USP Reference Standards are specified for use in conducting official USP–NF tests and assays. USP also provides Reference Standards specified in the Food Chemicals Codex as well as authentic substances—high-quality chemical samples—as a service to analytical, clinical, pharmaceutical and research laboratories. To confirm accuracy and reproducibility, USP Reference Standards are rigorously tested and evaluated by multiple independent laboratories including USP, commercial, regulatory, and academic labs. USP also provide publicly available, official documentary standards for pharmaceutical ingredients in the USP–NF that link directly with our primary reference standards.

UOM: 1 * 500 mg

Promo

Codice catalogo: (BOSSBS-13267R-CY7)

Fornitore: Bioss

Codice articolo fornitore: BS-13267R-CY7

Codice articolo locale: BOSSBS-13267R-CY7

Descrizione: GALK2 is important in the first step of the galactose metabolism pathway. GALK1, which belongs to the GHMP kinase family of proteins, is a crucial enzyme for galactose metabolism, specifically converting ?d-galactose to galactose 1-phosphate. Defects in the gene encoding GALK1 can cause galactosemia II, an autosomal recessive disorder characterized by congenital cataracts during infancy, often within the first two weeks of life. In the adult population, galactosemia II can cause presenile cataracts that are secondary to accumulation of galactitol in the lens of the eye. A second gene, GALK2, encodes an enzyme with greater activity against GalNAc than galactose. GALK2 has been implicated in the salvage pathway for the reutilization of free GalNAc derived from the degradation of complex carbohydrates.

UOM: 1 * 100 µl

Promo

Codice catalogo: (EDQMG0049000)

Fornitore: EDQM

Codice articolo fornitore: G0049000

Codice articolo locale: EDQMG0049000

Descrizione: Galactitol

UOM: 1 * 50 mg

Promo

Codice catalogo: (BOSSBS-13267R-A555)

Fornitore: Bioss

Codice articolo fornitore: BS-13267R-A555

Codice articolo locale: BOSSBS-13267R-A555

Descrizione: GALK2 is important in the first step of the galactose metabolism pathway. GALK1, which belongs to the GHMP kinase family of proteins, is a crucial enzyme for galactose metabolism, specifically converting ?d-galactose to galactose 1-phosphate. Defects in the gene encoding GALK1 can cause galactosemia II, an autosomal recessive disorder characterized by congenital cataracts during infancy, often within the first two weeks of life. In the adult population, galactosemia II can cause presenile cataracts that are secondary to accumulation of galactitol in the lens of the eye. A second gene, GALK2, encodes an enzyme with greater activity against GalNAc than galactose. GALK2 has been implicated in the salvage pathway for the reutilization of free GalNAc derived from the degradation of complex carbohydrates.

UOM: 1 * 100 µl

Promo

Codice catalogo: (BOSSBS-13267R-A647)

Fornitore: Bioss

Codice articolo fornitore: BS-13267R-A647

Codice articolo locale: BOSSBS-13267R-A647

Descrizione: GALK2 is important in the first step of the galactose metabolism pathway. GALK1, which belongs to the GHMP kinase family of proteins, is a crucial enzyme for galactose metabolism, specifically converting ?d-galactose to galactose 1-phosphate. Defects in the gene encoding GALK1 can cause galactosemia II, an autosomal recessive disorder characterized by congenital cataracts during infancy, often within the first two weeks of life. In the adult population, galactosemia II can cause presenile cataracts that are secondary to accumulation of galactitol in the lens of the eye. A second gene, GALK2, encodes an enzyme with greater activity against GalNAc than galactose. GALK2 has been implicated in the salvage pathway for the reutilization of free GalNAc derived from the degradation of complex carbohydrates.

UOM: 1 * 100 µl

Promo

Codice catalogo: (BOSSBS-13267R-A488)

Fornitore: Bioss

Codice articolo fornitore: BS-13267R-A488

Codice articolo locale: BOSSBS-13267R-A488

Descrizione: GALK2 is important in the first step of the galactose metabolism pathway. GALK1, which belongs to the GHMP kinase family of proteins, is a crucial enzyme for galactose metabolism, specifically converting ?d-galactose to galactose 1-phosphate. Defects in the gene encoding GALK1 can cause galactosemia II, an autosomal recessive disorder characterized by congenital cataracts during infancy, often within the first two weeks of life. In the adult population, galactosemia II can cause presenile cataracts that are secondary to accumulation of galactitol in the lens of the eye. A second gene, GALK2, encodes an enzyme with greater activity against GalNAc than galactose. GALK2 has been implicated in the salvage pathway for the reutilization of free GalNAc derived from the degradation of complex carbohydrates.

UOM: 1 * 100 µl

Promo