Hai cercato: Supplementi ed additivi per colture cellulari

Codice catalogo: (BOSSBS-15484R-CY7)

Fornitore: Bioss

Codice articolo fornitore: BS-15484R-CY7

Codice articolo locale: BOSSBS-15484R-CY7

Descrizione: HIBCH is a 386 amino acid protein belonging to the enoyl-CoA hydratase/isomerase family. Localising to the mitochondria, HIBCH is highly expressed in liver and kidney, with lower levels found in heart, muscle and brain. HIBCH hydrolyses HIBYL-CoA, a saline catabolite, and _-hydroxypropionyl-CoA, an intermediate in the minor pathway involved in the metabolism of proprionate. Existing as two alternatively spliced isoforms, the gene encoding HIBCH maps to human chromosome 2q32.2. Defects to this gene result in HIBCH deficiency (HIBCHD), known alternatively as deficiency of _-hydroxyisobutyryl CoA deacylase or methacrylic aciduria. HIBCHD is characterised by the accumulation of methacrylyl-CoA, a highly reactive compound that undergoes addition reactions with free sulfhydryl groups. Phenotypic symptoms include early deterioration of neurological function, delayed motor skill development and hypotonia.

UOM: 1 * 100 µl

Promo

Codice catalogo: (BOSSBS-15484R-CY5)

Fornitore: Bioss

Codice articolo fornitore: BS-15484R-CY5

Codice articolo locale: BOSSBS-15484R-CY5

Descrizione: HIBCH is a 386 amino acid protein belonging to the enoyl-CoA hydratase/isomerase family. Localising to the mitochondria, HIBCH is highly expressed in liver and kidney, with lower levels found in heart, muscle and brain. HIBCH hydrolyses HIBYL-CoA, a saline catabolite, and _-hydroxypropionyl-CoA, an intermediate in the minor pathway involved in the metabolism of proprionate. Existing as two alternatively spliced isoforms, the gene encoding HIBCH maps to human chromosome 2q32.2. Defects to this gene result in HIBCH deficiency (HIBCHD), known alternatively as deficiency of _-hydroxyisobutyryl CoA deacylase or methacrylic aciduria. HIBCHD is characterised by the accumulation of methacrylyl-CoA, a highly reactive compound that undergoes addition reactions with free sulfhydryl groups. Phenotypic symptoms include early deterioration of neurological function, delayed motor skill development and hypotonia.

UOM: 1 * 100 µl

Promo

Codice catalogo: (BOSSBS-15484R)

Fornitore: Bioss

Codice articolo fornitore: BS-15484R

Codice articolo locale: BOSSBS-15484R

Descrizione: HIBCH is a 386 amino acid protein belonging to the enoyl-CoA hydratase/isomerase family. Localizing to the mitochondria, HIBCH is highly expressed in liver and kidney, with lower levels found in heart, muscle and brain. HIBCH hydrolyzes HIBYL-CoA, a saline catabolite, and β-hydroxypropionyl-CoA, an intermediate in the minor pathway involved in the metabolism of proprionate. Existing as two alternatively spliced isoforms, the gene encoding HIBCH maps to human chromosome 2q32.2. Defects to this gene result in HIBCH deficiency (HIBCHD), known alternatively as deficiency of β-hydroxyisobutyryl CoA deacylase or methacrylic aciduria. HIBCHD is characterized by the accumulation of methacrylyl-CoA, a highly reactive compound that undergoes addition reactions with free sulfhydryl groups. Phenotypic symptoms include early deterioration of neurological function, delayed motor skill development and hypotonia.

UOM: 1 * 100 µl

Promo

Codice catalogo: (BOSSBS-15484R-A350)

Fornitore: Bioss

Codice articolo fornitore: BS-15484R-A350

Codice articolo locale: BOSSBS-15484R-A350

Descrizione: HIBCH is a 386 amino acid protein belonging to the enoyl-CoA hydratase/isomerase family. Localising to the mitochondria, HIBCH is highly expressed in liver and kidney, with lower levels found in heart, muscle and brain. HIBCH hydrolyses HIBYL-CoA, a saline catabolite, and _-hydroxypropionyl-CoA, an intermediate in the minor pathway involved in the metabolism of proprionate. Existing as two alternatively spliced isoforms, the gene encoding HIBCH maps to human chromosome 2q32.2. Defects to this gene result in HIBCH deficiency (HIBCHD), known alternatively as deficiency of _-hydroxyisobutyryl CoA deacylase or methacrylic aciduria. HIBCHD is characterised by the accumulation of methacrylyl-CoA, a highly reactive compound that undergoes addition reactions with free sulfhydryl groups. Phenotypic symptoms include early deterioration of neurological function, delayed motor skill development and hypotonia.

UOM: 1 * 100 µl

Promo

Fornitore: Apollo Scientific

Descrizione: 6-Propyl-2-thiouracil 97+%

Fornitore: Thermo Fisher Scientific

Descrizione: 6-Propyl-2-thiouracil ≥98%

Fornitore: Apollo Scientific

Descrizione: Propyl acetoacetate 95%

Codice catalogo: (APOSOR925076-5G)

Fornitore: Apollo Scientific

Codice articolo fornitore: OR925076-5G

Codice articolo locale: APOSOR925076-5G

Descrizione: 2-Propyl-2-oxazoline 95%

UOM: 1 * 5 g

Promo

Codice catalogo: (BOSSBS-15484R-FITC)

Fornitore: Bioss

Codice articolo fornitore: BS-15484R-FITC

Codice articolo locale: BOSSBS-15484R-FITC

Descrizione: HIBCH is a 386 amino acid protein belonging to the enoyl-CoA hydratase/isomerase family. Localising to the mitochondria, HIBCH is highly expressed in liver and kidney, with lower levels found in heart, muscle and brain. HIBCH hydrolyses HIBYL-CoA, a saline catabolite, and _-hydroxypropionyl-CoA, an intermediate in the minor pathway involved in the metabolism of proprionate. Existing as two alternatively spliced isoforms, the gene encoding HIBCH maps to human chromosome 2q32.2. Defects to this gene result in HIBCH deficiency (HIBCHD), known alternatively as deficiency of _-hydroxyisobutyryl CoA deacylase or methacrylic aciduria. HIBCHD is characterised by the accumulation of methacrylyl-CoA, a highly reactive compound that undergoes addition reactions with free sulfhydryl groups. Phenotypic symptoms include early deterioration of neurological function, delayed motor skill development and hypotonia.

UOM: 1 * 100 µl

Promo

Fornitore: TCI

Descrizione: 1-Propyl isothiocyanate ≥98.0% (by GC)

Fornitore: TCI

Descrizione: Propyl Levulinate ≥98.0% (by GC)

Fornitore: Thermo Fisher Scientific

Descrizione: 2-Propyl-1-heptanol ≥98%

MSDS Certificati

Fornitore: Thermo Fisher Scientific

Descrizione: 1-Propyl-4-ethynylbenzene ≥97%

MSDS

Codice catalogo: (TCIAI0108-25ML)

Fornitore: TCI

Codice articolo fornitore: I0108-25ML

Codice articolo locale: TCIAI0108-25ML

Descrizione: Propyl isobutyrate ≥97.0% (by GC)

UOM: 1 * 25 mL

Promo

Codice catalogo: (BOSSBS-15484R-HRP)

Fornitore: Bioss

Codice articolo fornitore: BS-15484R-HRP

Codice articolo locale: BOSSBS-15484R-HRP

Descrizione: HIBCH is a 386 amino acid protein belonging to the enoyl-CoA hydratase/isomerase family. Localising to the mitochondria, HIBCH is highly expressed in liver and kidney, with lower levels found in heart, muscle and brain. HIBCH hydrolyses HIBYL-CoA, a saline catabolite, and _-hydroxypropionyl-CoA, an intermediate in the minor pathway involved in the metabolism of proprionate. Existing as two alternatively spliced isoforms, the gene encoding HIBCH maps to human chromosome 2q32.2. Defects to this gene result in HIBCH deficiency (HIBCHD), known alternatively as deficiency of _-hydroxyisobutyryl CoA deacylase or methacrylic aciduria. HIBCHD is characterised by the accumulation of methacrylyl-CoA, a highly reactive compound that undergoes addition reactions with free sulfhydryl groups. Phenotypic symptoms include early deterioration of neurological function, delayed motor skill development and hypotonia.

UOM: 1 * 100 µl

Promo

Fornitore: Thermo Fisher Scientific

Descrizione: 1-Propyl-2-thiourea ≥98%

MSDS Certificati