Hai cercato: Dimethyl+fumarate

Codice catalogo: (BOSSBS-12515R-A350)

Fornitore: Bioss

Codice articolo fornitore: BS-12515R-A350

Codice articolo locale: BOSSBS-12515R-A350

Descrizione: ASL is a member of the lyase 1 family of proteins and is predominantly expressed in the liver. Localizing to the cytoplasm and existing as a homotetramer, ASL catalyzes the hydrolytic cleavage of argininosuccinic acid (ASA) to fumarate and arginine, an essential step of the urea cycle which is crucial for the detoxification of ammonia. This reaction is also involved in the biosynthesis of arginine. In addition, ASL shares high sequence homology with the avian and reptilian eye lens protein, d-crystallin. Mutations in the gene encoding ASL leads to an accumulation of ASA in body fluids and results in Arginosuc-cinic aciduria (ASAuria), an autosomal recessive disorder that is characterized by hyperammonemia, liver enlargement, convulsions, physical and mental retardation, episodic unconsciousness and dry and brittle hair showing trich-orrhexis nodosa (weak points or nodes in the hair shaft).

UOM: 1 * 100 µl

Promo

Codice catalogo: (BOSSBS-12515R-HRP)

Fornitore: Bioss

Codice articolo fornitore: BS-12515R-HRP

Codice articolo locale: BOSSBS-12515R-HRP

Descrizione: ASL is a member of the lyase 1 family of proteins and is predominantly expressed in the liver. Localizing to the cytoplasm and existing as a homotetramer, ASL catalyzes the hydrolytic cleavage of argininosuccinic acid (ASA) to fumarate and arginine, an essential step of the urea cycle which is crucial for the detoxification of ammonia. This reaction is also involved in the biosynthesis of arginine. In addition, ASL shares high sequence homology with the avian and reptilian eye lens protein, d-crystallin. Mutations in the gene encoding ASL leads to an accumulation of ASA in body fluids and results in Arginosuc-cinic aciduria (ASAuria), an autosomal recessive disorder that is characterized by hyperammonemia, liver enlargement, convulsions, physical and mental retardation, episodic unconsciousness and dry and brittle hair showing trich-orrhexis nodosa (weak points or nodes in the hair shaft).

UOM: 1 * 100 µl

Promo

Fornitore: Thermo Fisher Scientific

Descrizione: Ketotifen fumarate 99%

MSDS Certificati

Codice catalogo: (BOSSBS-12515R-FITC)

Fornitore: Bioss

Codice articolo fornitore: BS-12515R-FITC

Codice articolo locale: BOSSBS-12515R-FITC

Descrizione: ASL is a member of the lyase 1 family of proteins and is predominantly expressed in the liver. Localizing to the cytoplasm and existing as a homotetramer, ASL catalyzes the hydrolytic cleavage of argininosuccinic acid (ASA) to fumarate and arginine, an essential step of the urea cycle which is crucial for the detoxification of ammonia. This reaction is also involved in the biosynthesis of arginine. In addition, ASL shares high sequence homology with the avian and reptilian eye lens protein, d-crystallin. Mutations in the gene encoding ASL leads to an accumulation of ASA in body fluids and results in Arginosuc-cinic aciduria (ASAuria), an autosomal recessive disorder that is characterized by hyperammonemia, liver enlargement, convulsions, physical and mental retardation, episodic unconsciousness and dry and brittle hair showing trich-orrhexis nodosa (weak points or nodes in the hair shaft).

UOM: 1 * 100 µl

Promo

Codice catalogo: (PROOLGCFOR0394.00)

Fornitore: LGC Standards PROMOCHEM

Codice articolo fornitore: LGCFOR0394.00

Codice articolo locale: PROOLGCFOR0394.00

Descrizione: Organic Standard, Tiamulin hydrogen fumarate

UOM: 1 * 10 mg

Promo

Codice catalogo: (PROOMM1329.00)

Fornitore: LGC Standards PROMOCHEM

Codice articolo fornitore: MM1329.00

Codice articolo locale: PROOMM1329.00

Descrizione: Organic Standard, Tenofovir disoproxil fumarate

UOM: 1 * 100 mg

Promo

Codice catalogo: (EDQMY0000333)

Fornitore: EDQM

Codice articolo fornitore: Y0000333

Codice articolo locale: EDQMY0000333

Descrizione: Organic Standard, Tiamulin hydrogen fumarate, Tipo di conf.: Vial

UOM: 1 * 500 mg

Promo

Fornitore: LGC Standards PROMOCHEM

Descrizione: Organic Standard, 3-ethyl 5-methyl 2-[(2-aminoethoxy)methyl]-4-(2-chlorophenyl)-6-methylpyridine-3,5-dicarboxylate fumarate

Codice catalogo: (EHERC12606600)

Fornitore: EHRENSTORFER

Codice articolo fornitore: C12606600

Codice articolo locale: EHERC12606600

Descrizione: Dietil fumarato

UOM: 1 * 0,25 g

Promo

Codice catalogo: (EDQMY0001657)

Fornitore: EDQM

Codice articolo fornitore: Y0001657

Codice articolo locale: EDQMY0001657

Descrizione: Organic Standard, Quetiapine fumarate

UOM: 1 * 50 mg

Promo

Fornitore: Spectrum Chemical

Descrizione: BSE/TSE statement (available upon request)
Allergen statement (available upon request)

Codice catalogo: (PROOMM0386.12)

Fornitore: LGC Standards PROMOCHEM

Codice articolo fornitore: MM0386.12

Codice articolo locale: PROOMM0386.12

Descrizione: Organic Standard, 3-Ethyl 5-methyl 2-[(2-aminoethoxy)methyl]-4-(2-chlorophenyl)-6-methylpyridine-3,5-dicarboxylate fumarate

UOM: 1 * 100 mg

Promo

Codice catalogo: (EHERC13955500)

Fornitore: EHRENSTORFER

Codice articolo fornitore: C13955500

Codice articolo locale: EHERC13955500

Descrizione: Acido fumarico

UOM: 1 * 0,25 g

Certificati Promo

Fornitore: MERCK PRODUCTION CHEMICALS

Descrizione: Acido fumarico NF, SAFC®

MSDS Certificati

Codice catalogo: (PRSI91-668)

Fornitore: ProSci Inc.

Codice articolo fornitore: 91-668

Codice articolo locale: PRSI91-668

Descrizione: Fumarylacetoacetase belongs to the FAH family. Fumarylacetoacetase is primary expressed in liver and kidney. It exists as a homodimer and catalyses the hydrolysis of 4-fumarylacetoacetate into fumarate and acetoacetate. Defects in Fumarylacetoacetase cause tyrosinemia type 1, which is congenital metabolism defect characterised by elevated levels of tyrosine in the blood and urine, and hepatorenal manifestations. Typical features include renal tubular injury, self-mutilation, hepatic necrosis, episodic weakness, and seizures.

UOM: 1 * 50 µG

Promo

Fornitore: Thermo Fisher Scientific

Descrizione: Thiabendazole, a metal chelator and helminth-specific fumarate reductase inhibitor, is used primarily as an anthelmintic to control infections by helminth organisms.

MSDS Certificati