Hai cercato: Coenzyme+B12

Codice catalogo: (BOSSBS-5018R-CY7)

Fornitore: Bioss

Codice articolo fornitore: BS-5018R-CY7

Codice articolo locale: BOSSBS-5018R-CY7

Descrizione: ACADVL (acyl-Coenzyme A dehydrogenase, very long chain) catalyzes the first step of the mitochondrial fatty acid beta-oxidation pathway. It is specific to esters of long-chain and very long chain fatty acids such as palmitoyl-CoA and stearoyl-CoA. Deficiencies in ACADVL are associated with reduced myocardial fatty acid beta-oxidation and cardiomyopathy.

UOM: 1 * 100 µl

Promo

Codice catalogo: (BOSSBS-8340R-CY5)

Fornitore: Bioss

Codice articolo fornitore: BS-8340R-CY5

Codice articolo locale: BOSSBS-8340R-CY5

Descrizione: PANK4 belongs to the pantothenate kinase family. Pantothenate kinase is a key regulatory enzyme in the physiological regulation of the intracellular coenzyme A (CoA) concentration. It catalyzes the first committed step in the universal biosynthetic pathway leading to CoA and is itself subject to regulation through feedback inhibition by CoA. This family member is most abundant in muscle but is expressed in all tissues.

UOM: 1 * 100 µl

Promo

Codice catalogo: (BOSSBS-4047R)

Fornitore: Bioss

Codice articolo fornitore: BS-4047R

Codice articolo locale: BOSSBS-4047R

Descrizione: ACADM protein is a medium chain specific (C4 to C12 straight chain) acyl Coenzyme A dehydrogenase. The enzyme catalyzes the initial step of the mitochondrial fatty acid beta oxidation pathway. ACADM expression is induced during periods of fasting, when reliance on fatty acids for energy is increased. Clinical phenotypes are associated with ACADM hereditary deficiency.

UOM: 1 * 100 µl

Promo

Codice catalogo: (BOSSBS-4047R-A350)

Fornitore: Bioss

Codice articolo fornitore: BS-4047R-A350

Codice articolo locale: BOSSBS-4047R-A350

Descrizione: ACADM protein is a medium chain specific (C4 to C12 straight chain) acyl Coenzyme A dehydrogenase. The enzyme catalyzes the initial step of the mitochondrial fatty acid beta oxidation pathway. ACADM expression is induced during periods of fasting, when reliance on fatty acids for energy is increased. Clinical phenotypes are associated with ACADM hereditary deficiency.

UOM: 1 * 100 µl

Promo

Codice catalogo: (BOSSBS-4047R-CY7)

Fornitore: Bioss

Codice articolo fornitore: BS-4047R-CY7

Codice articolo locale: BOSSBS-4047R-CY7

Descrizione: ACADM protein is a medium chain specific (C4 to C12 straight chain) acyl Coenzyme A dehydrogenase. The enzyme catalyzes the initial step of the mitochondrial fatty acid beta oxidation pathway. ACADM expression is induced during periods of fasting, when reliance on fatty acids for energy is increased. Clinical phenotypes are associated with ACADM hereditary deficiency.

UOM: 1 * 100 µl

Promo

Codice catalogo: (BOSSBS-4047R-CY3)

Fornitore: Bioss

Codice articolo fornitore: BS-4047R-CY3

Codice articolo locale: BOSSBS-4047R-CY3

Descrizione: ACADM protein is a medium chain specific (C4 to C12 straight chain) acyl Coenzyme A dehydrogenase. The enzyme catalyzes the initial step of the mitochondrial fatty acid beta oxidation pathway. ACADM expression is induced during periods of fasting, when reliance on fatty acids for energy is increased. Clinical phenotypes are associated with ACADM hereditary deficiency.

UOM: 1 * 100 µl

Promo

Codice catalogo: (BOSSBS-8340R-CY3)

Fornitore: Bioss

Codice articolo fornitore: BS-8340R-CY3

Codice articolo locale: BOSSBS-8340R-CY3

Descrizione: PANK4 belongs to the pantothenate kinase family. Pantothenate kinase is a key regulatory enzyme in the physiological regulation of the intracellular coenzyme A (CoA) concentration. It catalyzes the first committed step in the universal biosynthetic pathway leading to CoA and is itself subject to regulation through feedback inhibition by CoA. This family member is most abundant in muscle but is expressed in all tissues.

UOM: 1 * 100 µl

Promo

Codice catalogo: (BOSSBS-8340R-CY5.5)

Fornitore: Bioss

Codice articolo fornitore: BS-8340R-CY5.5

Codice articolo locale: BOSSBS-8340R-CY5.5

Descrizione: PANK4 belongs to the pantothenate kinase family. Pantothenate kinase is a key regulatory enzyme in the physiological regulation of the intracellular coenzyme A (CoA) concentration. It catalyzes the first committed step in the universal biosynthetic pathway leading to CoA and is itself subject to regulation through feedback inhibition by CoA. This family member is most abundant in muscle but is expressed in all tissues.

UOM: 1 * 100 µl

Promo

Codice catalogo: (BOSSBS-6551R-CY5)

Fornitore: Bioss

Codice articolo fornitore: BS-6551R-CY5

Codice articolo locale: BOSSBS-6551R-CY5

Descrizione: NADH:ubiquinone oxidoreductase (complex I) catalyzes the transfer of electrons from NADH to ubiquinone (coenzyme Q) in the first step of the mitochondrial respiratory chain, resulting in the translocation of protons across the inner mitochondrial membrane. This gene encodes a complex I assembly factor. Mutations in this gene cause progressive encephalopathy resulting from mitochondrial complex I deficiency.

UOM: 1 * 100 µl

Promo

Codice catalogo: (PRSI30-414)

Fornitore: ProSci Inc.

Codice articolo fornitore: 30-414

Codice articolo locale: PRSI30-414

Descrizione: OXCT1 is a member of the 3-oxoacid CoA-transferase gene family. It is a homodimeric mitochondrial matrix enzyme that plays a central role in extrahepatic ketone body catabolism by catalyzing the reversible transfer of coenzyme A from succinyl-CoA to acetoacetate.This gene encodes a member of the 3-oxoacid CoA-transferase gene family. The encoded protein is a homodimeric mitochondrial matrix enzyme that plays a central role in extrahepatic ketone body catabolism by catalyzing the reversible transfer of coenzyme A from succinyl-CoA to acetoacetate. Mutations in this gene are associated with succinyl CoA:3-oxoacid CoA transferase deficiency.

UOM: 1 * 50 µG

Promo

Codice catalogo: (BOSSBS-8340R-CY7)

Fornitore: Bioss

Codice articolo fornitore: BS-8340R-CY7

Codice articolo locale: BOSSBS-8340R-CY7

Descrizione: PANK4 belongs to the pantothenate kinase family. Pantothenate kinase is a key regulatory enzyme in the physiological regulation of the intracellular coenzyme A (CoA) concentration. It catalyzes the first committed step in the universal biosynthetic pathway leading to CoA and is itself subject to regulation through feedback inhibition by CoA. This family member is most abundant in muscle but is expressed in all tissues.

UOM: 1 * 100 µl

Promo

Codice catalogo: (BOSSBS-4047R-A488)

Fornitore: Bioss

Codice articolo fornitore: BS-4047R-A488

Codice articolo locale: BOSSBS-4047R-A488

Descrizione: ACADM protein is a medium chain specific (C4 to C12 straight chain) acyl Coenzyme A dehydrogenase. The enzyme catalyzes the initial step of the mitochondrial fatty acid beta oxidation pathway. ACADM expression is induced during periods of fasting, when reliance on fatty acids for energy is increased. Clinical phenotypes are associated with ACADM hereditary deficiency.

UOM: 1 * 100 µl

Promo

Codice catalogo: (BOSSBS-6551R-A680)

Fornitore: Bioss

Codice articolo fornitore: BS-6551R-A680

Codice articolo locale: BOSSBS-6551R-A680

Descrizione: NADH:ubiquinone oxidoreductase (complex I) catalyzes the transfer of electrons from NADH to ubiquinone (coenzyme Q) in the first step of the mitochondrial respiratory chain, resulting in the translocation of protons across the inner mitochondrial membrane. This gene encodes a complex I assembly factor. Mutations in this gene cause progressive encephalopathy resulting from mitochondrial complex I deficiency.

UOM: 1 * 100 µl

Promo

Codice catalogo: (BOSSBS-5018R-CY3)

Fornitore: Bioss

Codice articolo fornitore: BS-5018R-CY3

Codice articolo locale: BOSSBS-5018R-CY3

Descrizione: ACADVL (acyl-Coenzyme A dehydrogenase, very long chain) catalyzes the first step of the mitochondrial fatty acid beta-oxidation pathway. It is specific to esters of long-chain and very long chain fatty acids such as palmitoyl-CoA and stearoyl-CoA. Deficiencies in ACADVL are associated with reduced myocardial fatty acid beta-oxidation and cardiomyopathy.

UOM: 1 * 100 µl

Promo

Codice catalogo: (BOSSBS-5018R-CY5)

Fornitore: Bioss

Codice articolo fornitore: BS-5018R-CY5

Codice articolo locale: BOSSBS-5018R-CY5

Descrizione: ACADVL (acyl-Coenzyme A dehydrogenase, very long chain) catalyzes the first step of the mitochondrial fatty acid beta-oxidation pathway. It is specific to esters of long-chain and very long chain fatty acids such as palmitoyl-CoA and stearoyl-CoA. Deficiencies in ACADVL are associated with reduced myocardial fatty acid beta-oxidation and cardiomyopathy.

UOM: 1 * 100 µl

Promo

Codice catalogo: (BOSSBS-5018R-A350)

Fornitore: Bioss

Codice articolo fornitore: BS-5018R-A350

Codice articolo locale: BOSSBS-5018R-A350

Descrizione: ACADVL (acyl-Coenzyme A dehydrogenase, very long chain) catalyzes the first step of the mitochondrial fatty acid beta-oxidation pathway. It is specific to esters of long-chain and very long chain fatty acids such as palmitoyl-CoA and stearoyl-CoA. Deficiencies in ACADVL are associated with reduced myocardial fatty acid beta-oxidation and cardiomyopathy.

UOM: 1 * 100 µl

Promo