Hai cercato: Coenzyme+B12

Codice catalogo: (BOSSBS-5018R-A350)

Fornitore: Bioss

Codice articolo fornitore: BS-5018R-A350

Codice articolo locale: BOSSBS-5018R-A350

Descrizione: ACADVL (acyl-Coenzyme A dehydrogenase, very long chain) catalyzes the first step of the mitochondrial fatty acid beta-oxidation pathway. It is specific to esters of long-chain and very long chain fatty acids such as palmitoyl-CoA and stearoyl-CoA. Deficiencies in ACADVL are associated with reduced myocardial fatty acid beta-oxidation and cardiomyopathy.

UOM: 1 * 100 µl

Promo

Codice catalogo: (BOSSBS-5018R-CY5.5)

Fornitore: Bioss

Codice articolo fornitore: BS-5018R-CY5.5

Codice articolo locale: BOSSBS-5018R-CY5.5

Descrizione: ACADVL (acyl-Coenzyme A dehydrogenase, very long chain) catalyzes the first step of the mitochondrial fatty acid beta-oxidation pathway. It is specific to esters of long-chain and very long chain fatty acids such as palmitoyl-CoA and stearoyl-CoA. Deficiencies in ACADVL are associated with reduced myocardial fatty acid beta-oxidation and cardiomyopathy.

UOM: 1 * 100 µl

Promo

Codice catalogo: (BOSSBS-8340R-A555)

Fornitore: Bioss

Codice articolo fornitore: BS-8340R-A555

Codice articolo locale: BOSSBS-8340R-A555

Descrizione: PANK4 belongs to the pantothenate kinase family. Pantothenate kinase is a key regulatory enzyme in the physiological regulation of the intracellular coenzyme A (CoA) concentration. It catalyzes the first committed step in the universal biosynthetic pathway leading to CoA and is itself subject to regulation through feedback inhibition by CoA. This family member is most abundant in muscle but is expressed in all tissues.

UOM: 1 * 100 µl

Promo

Codice catalogo: (PRSI90-352)

Fornitore: ProSci Inc.

Codice articolo fornitore: 90-352

Codice articolo locale: PRSI90-352

Descrizione: NAD kinase catalyses the transfer of a phosphate group from ATP to NAD+ to generate NADP+, which in its reduced form acts as an electron donor for biosynthetic reactions. NADP+ is an essential coenzyme in metabolism and provides reducing power to biosynthetic processes such as fatty acid biosynthesis.

UOM: 1 * 50 µG

Promo

Codice catalogo: (PRSI30-101)

Fornitore: ProSci Inc.

Codice articolo fornitore: 30-101

Codice articolo locale: PRSI30-101

Descrizione: ECHS1 functions in the second step of the mitochondrial fatty acid beta-oxidation pathway. It catalyzes the hydration of 2-trans-enoyl-coenzyme A (CoA) intermediates to L-3-hydroxyacyl-CoAs. ECHS1 is a member of the hydratase/isomerase superfamily. It localizes to the mitochondrial matrix.The protein encoded by this gene functions in the second step of the mitochondrial fatty acid beta-oxidation pathway. It catalyzes the hydration of 2-trans-enoyl-coenzyme A (CoA) intermediates to L-3-hydroxyacyl-CoAs. The gene product is a member of the hydratase/isomerase superfamily. It localizes to the mitochondrial matrix. Transcript variants utilizing alternative transcription initiation sites have been described in the literature.

UOM: 1 * 100 µG

Promo

Codice catalogo: (BOSSBS-4047R-A750)

Fornitore: Bioss

Codice articolo fornitore: BS-4047R-A750

Codice articolo locale: BOSSBS-4047R-A750

Descrizione: ACADM protein is a medium chain specific (C4 to C12 straight chain) acyl Coenzyme A dehydrogenase. The enzyme catalyses the initial step of the mitochondrial fatty acid beta oxidation pathway. ACADM expression is induced during periods of fasting, when reliance on fatty acids for energy is increased. Clinical phenotypes are associated with ACADM hereditary deficiency.

UOM: 1 * 100 µl

Promo

Codice catalogo: (BOSSBS-4047R-HRP)

Fornitore: Bioss

Codice articolo fornitore: BS-4047R-HRP

Codice articolo locale: BOSSBS-4047R-HRP

Descrizione: ACADM protein is a medium chain specific (C4 to C12 straight chain) acyl Coenzyme A dehydrogenase. The enzyme catalyzes the initial step of the mitochondrial fatty acid beta oxidation pathway. ACADM expression is induced during periods of fasting, when reliance on fatty acids for energy is increased. Clinical phenotypes are associated with ACADM hereditary deficiency.

UOM: 1 * 100 µl

Promo

Codice catalogo: (BOSSBS-8340R-HRP)

Fornitore: Bioss

Codice articolo fornitore: BS-8340R-HRP

Codice articolo locale: BOSSBS-8340R-HRP

Descrizione: PANK4 belongs to the pantothenate kinase family. Pantothenate kinase is a key regulatory enzyme in the physiological regulation of the intracellular coenzyme A (CoA) concentration. It catalyzes the first committed step in the universal biosynthetic pathway leading to CoA and is itself subject to regulation through feedback inhibition by CoA. This family member is most abundant in muscle but is expressed in all tissues.

UOM: 1 * 100 µl

Promo

Codice catalogo: (BOSSBS-8340R-A750)

Fornitore: Bioss

Codice articolo fornitore: BS-8340R-A750

Codice articolo locale: BOSSBS-8340R-A750

Descrizione: PANK4 belongs to the pantothenate kinase family. Pantothenate kinase is a key regulatory enzyme in the physiological regulation of the intracellular coenzyme A (CoA) concentration. It catalyzes the first committed step in the universal biosynthetic pathway leading to CoA and is itself subject to regulation through feedback inhibition by CoA. This family member is most abundant in muscle but is expressed in all tissues.

UOM: 1 * 100 µl

Promo

Codice catalogo: (BOSSBS-8340R-A647)

Fornitore: Bioss

Codice articolo fornitore: BS-8340R-A647

Codice articolo locale: BOSSBS-8340R-A647

Descrizione: PANK4 belongs to the pantothenate kinase family. Pantothenate kinase is a key regulatory enzyme in the physiological regulation of the intracellular coenzyme A (CoA) concentration. It catalyzes the first committed step in the universal biosynthetic pathway leading to CoA and is itself subject to regulation through feedback inhibition by CoA. This family member is most abundant in muscle but is expressed in all tissues.

UOM: 1 * 100 µl

Promo

Codice catalogo: (PRSI55-878)

Fornitore: ProSci Inc.

Codice articolo fornitore: 55-878

Codice articolo locale: PRSI55-878

Descrizione: Coenzyme A diphosphatase that mediates the hydrolysis of a wide range of CoA esters, including choloyl-CoA and branched-chain fatty-acyl-CoA esters. At low substrate concentrations medium and long-chain fatty-acyl-CoA esters are the primary substrates (By similarity).

UOM: 1 * 400 µl

Promo

Codice catalogo: (PRSI30-708)

Fornitore: ProSci Inc.

Codice articolo fornitore: 30-708

Codice articolo locale: PRSI30-708

Descrizione: NAGS is a mitochondrial enzyme that catalyzes the formation of N-acetylglutamate (NAG) from glutamate and acetyl coenzyme-A. NAG is a cofactor of carbamyl phosphate synthetase I (CPSI), the first enzyme of the urea cycle in mammals. Deficiencies in N-acetylglutamate synthase have been associated with hyperammonemia.The N-acetylglutamate synthase gene encodes a mitochondrial enzyme that catalyzes the formation of N-acetylglutamate (NAG) from glutamate and acetyl coenzyme-A. NAG is a cofactor of carbamyl phosphate synthetase I (CPSI), the first enzyme of the urea cycle in mammals. This gene may regulate ureagenesis by altering NAG availability and, thereby, CPSI activity. Deficiencies in N-acetylglutamate synthase have been associated with hyperammonemia.

UOM: 1 * 100 µG

Promo

Codice catalogo: (PRSI30-102)

Fornitore: ProSci Inc.

Codice articolo fornitore: 30-102

Codice articolo locale: PRSI30-102

Descrizione: ECHS1 functions in the second step of the mitochondrial fatty acid beta-oxidation pathway. It catalyzes the hydration of 2-trans-enoyl-coenzyme A (CoA) intermediates to L-3-hydroxyacyl-CoAs. ECHS1 is a member of the hydratase/isomerase superfamily. It localizes to the mitochondrial matrix.The protein encoded by this gene functions in the second step of the mitochondrial fatty acid beta-oxidation pathway. It catalyzes the hydration of 2-trans-enoyl-coenzyme A (CoA) intermediates to L-3-hydroxyacyl-CoAs. The gene product is a member of the hydratase/isomerase superfamily. It localizes to the mitochondrial matrix. Transcript variants utilizing alternative transcription initiation sites have been described in the literature.

UOM: 1 * 100 µG

Promo

Codice catalogo: (PRSI90-353)

Fornitore: ProSci Inc.

Codice articolo fornitore: 90-353

Codice articolo locale: PRSI90-353

Descrizione: NAD kinase catalyses the transfer of a phosphate group from ATP to NAD+ to generate NADP+, which in its reduced form acts as an electron donor for biosynthetic reactions. NADP+ is an essential coenzyme in metabolism and provides reducing power to biosynthetic processes such as fatty acid biosynthesis.

UOM: 1 * 50 µG

Promo

Fornitore: MP Biomedicals

Descrizione: Major electron acceptor molecule in biological oxidations. Acts as a coenzyme for hydride-transfer enzymes and a substrate for NAD(+)-consuming enzymes, which include ADP-ribose transferases, poly(ADP-ribose) polymerases, cADP-ribose synthases and sirtuins. Recently reported to be a P2Y11 agonist.

Codice catalogo: (PRSI56-779)

Fornitore: ProSci Inc.

Codice articolo fornitore: 56-779

Codice articolo locale: PRSI56-779

Descrizione: NADH:ubiquinone oxidoreductase (complex I) catalyzes the transfer of electrons from NADH to ubiquinone (coenzyme Q) in the first step of the mitochondrial respiratory chain, resulting in the translocation of protons across the inner mitochondrial membrane. This gene encodes a complex I assembly factor. Mutations in this gene are a cause of mitochondrial complex I deficiency. [provided by RefSeq].

UOM: 1 * 400 µl

Promo